منابع مشابه
Case Report - Scleromyxedema : An Atypical Form in a 50 Years Old Male Patient
Scleromyxedema is a chronic, progressive condition characterised by dermal fibrosis and mucinosis. The clinical variants consist of generalised confluent lichenoid eruptions (scleromyxedema) with systemic manifestations and a localised variant with discrete papular eruptions. The cases which do not fit into either of the category are termed as atypical or intermediate form. We report such a cas...
متن کاملParaneoplastic atypical scleromyxedema with advanced gastric cancer
INTRODUCTION Scleromyxedema is a rare, chronic and progressive disorder of unknown origin characterized by a generalized papular eruption and sclerodermoid induration, with histopathologic features of mucin deposition and fibroblast proliferation. The disease is usually associated with a monoclonal gammopathy. However, only a few cases associated with neoplasms have been reported. We report a c...
متن کاملA Case of Autoimmune Polyglandular Syndrome .ype 2 Associated with Atypical Form of Scleromyxedema
BACKGROUND Autoimmune polyglandular syndrome type 2 represents an uncommon endocrine disorder composed by Addison's disease with autoimmune thyroid disease (Schmidt's syndrome) and/or type 1 diabetes mellitus. Scleromyxedema is a rare progressive cutaneous mucinosis usually associated with systemic involvement and paraproteinemia. To the best of our knowledge, there is no case report of Schmidt...
متن کاملAtypical scleromyxedema presenting with cutaneous and cardiovascular manifestations
Scleromyxedema is part of a group of cutaneous mucinoses, characterized by a generalized papular eruption, dermal mucin deposition, and an increase in dermal collagen. This condition can be localized as discrete papular lichen myxedematous skin or as a systemic condition usually associated with paraproteinaemia. To date, there is no unifying treatment and is limited by rarity, small number of c...
متن کاملAnterior Plagiocephaly in an Atypical Case of Apert Syndrome
Apert syndrome is a congenital craniosynostosis syndrome comprising of bilateral coronal synostosis , symmetric syndactyly of hands and feet and midface hypoplasia. We present an atypical phenotype of this syndrome with right sided unilateral coronal synostosis. However, type I apert hand and other clinical and radiological features suggestthe diagnosis. Genetic analysis revealed an absence of ...
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ژورنال
عنوان ژورنال: Indian Journal of Dermatology
سال: 2015
ISSN: 0019-5154
DOI: 10.4103/0019-5154.156456